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Liver Transplant Outcomes / Quality Measures

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Primary Diagnoses for Patients Receiving Liver Transplants

The primary diagnoses for patients receiving liver transplants at the Pediatric Liver Care Center at Cincinnati Children's Hospital Medical Center are:

Diagnosis% of Overall Liver Transplant Volume

Cholestatic

(Alagille Syndrome, Biliary Atresia, Idiopathic Cholestasis, Primary Schlerosing Cholangitis, TPN Induced)

51%

Metabolic

(Antitrypsin Deficiency, Citrulinemia, Glycogen Storage Disease, Neonatal Hemachromatosis, OTC deficiency, Primary Hyper Oxaluria, Tyrosinemia, Urea Cycle Defects, Wilson's Disease)

17%

Acute Liver Failure

(Viral infection, drug toxicity, autoimmune disorders, indeterminate)

15%

Cirrhosis

(Autoimmune Hepatitis, Cryptogenic Cirrhosis, Neonatal Hepatitis)

8%

Tumor

(Hepatoblastoma, Hepatocellular Carcinoma, Hemangioendothelioma)

4%

Other

(Short Gut, Budd-Chiari Syndrome, Abernathy's Syndrome and other diseases that don't fall in any of the above categories)

5%