Cincinnati Children's Hospital Medical Center Logo

Liver Transplant Frequent Questions

What Are the Primary Diagnoses for Patients Receiving Liver Transplants?

The primary diagnoses for patients receiving liver transplants at the Liver Care Center at Cincinnati Children's Hospital Medical Center are:

Diagnosis% of Overall Liver Transplant Volume

Cholestatic

(Alagille Syndrome, Biliary Atresia, Idiopathic Cholestasis, Primary Schlerosing Cholangitis, TPN Induced)

51%

Metabolic

(Antitrypsin Deficiency, Citrulinemia, Glycogen Storage Disease, Neonatal Hemachromatosis, OTC deficiency, Primary Hyper Oxaluria, Tyrosinemia, Urea Cycle Defects, Wilson's Disease)

17%

Acute Liver Failure

(Viral infection, drug toxicity, autoimmune disorders, indeterminate)

15%

Cirrhosis

(Autoimmune Hepatitis, Cryptogenic Cirrhosis, Neonatal Hepatitis)

8%

Tumor

(Hepatoblastoma, Hepatocellular Carcinoma, Hemangioendothelioma)

4%

Other

(Short Gut, Budd-Chiari Syndrome, Abernathy's Syndrome and other diseases that don't fall in any of the above categories)

5%
Data source: Liver Care Center Team, Cincinnati Children's, March 2005