Summary Page Hypoplastic Left Heart Syndrome
Hypoplastic Left Heart Syndrome
- Hypoplastic ascending aorta and aortic arch.
- Hypoplastic left ventricle.
- Large patent ductus arteriosus supplying the only source of blood flow to the body.
- Atrial septal defect allowing blood returning from lungs to reach the single ventricle.
- The PDA has been ligated and the hypoplastic aorta is opened longitudinally from the descending aorta to near its origin at the heart.
- The main pulmonary artery has been divided and the distal end closed.
- A Gore-tex™ modified Blalock-Taussig shunt from the innominate artery to the right pulmonary artery supplies blood flow to the lungs.
- The aorta has been reconstructed using the proximal main pulmonary artery, the hypoplastic aorta, and a patch so that the single right ventricle now ejects primarily to the body.
HLHS Repair - step 1
HLHS Repair - completed