Fibrosarcoma in Children

Fibrosarcoma is a rare, malignant (cancerous) type of soft tissue sarcoma that occurs most commonly in infants and young children under 5 years of age and in patients 10 to 15 years old.

Like other sarcomas, fibrosarcoma occurs wherever fibrous tissues are found, and involves the extremities and deeper structures of the body. This type of cancer most commonly affects the limbs and the trunk of the body, but it can occur anywhere.

The symptoms depend on the area of the body where the tumor is located but usually include a swelling or lump.

Diagnosis of fibrosarcoma is made by biopsy of the tumor. This is a surgical procedure done under general anesthesia so the child is not conscious and will not feel any pain. The suspicious mass or pieces of it are removed and looked at under a microscope.

Other tests may be performed to see if the disease has spread including a CT scan, MRI, radioisotope scans and/or a bone marrow aspirate.  These tests provide information about the stage of the cancer, and an indication of how far the cancer may have spread.

A combination of surgery, chemotherapy and radiation is most often used.

The child's treatment plan will be based on the location of the tumor and whether the tumor has spread, your child’s age, overall health and medical history, your child’s tolerance for specific medications and procedures, and your opinions / preferences.

The prognosis for fibrosarcoma is related to the age of the patient (infant vs. others), location of the tumor if the tumor has spread, and if the tumor was completely removed at the time of surgery. With combined treatment survival rates are improving.

Cincinnati Children's is an international referral center for the treatment of children and young adults with high-risk and relapsed cancers. Our faculty members lead national efforts in the development of new targeted therapies, immunological approaches, and stem cell transplantation. 

Learn more about active treatment regimens for relapsed fibrosarcoma.

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Last Updated 10/2015