Pectus Carinatum Causes
The cause of Pectus Carinatum is currently unknown, but the fact that it tends to recur in families suggests that genetics may play a role.
Excessive growth and structural abnormalities of cartilage (tough, connective tissue) of the ribs and breastbone are present in pectus carinatum.
Signs and Symptoms of Pectus Carinatum
For the most part, children with pectus carinatum do not have symptoms. If symptoms are present, they are typically mild and limited to occasional chest wall pain and tenderness. However the psychosocial impact may be difficult for the child. Patients with pectus carinatum frequently suffer from a poor body image and low self-esteem.
Some children with pectus carinatum also have scoliosis (sideways curvature of the spine), kyphosis (outward curvature of the spine) or connective tissue diseases such as Ehlers-Danlos and Marfan syndromes.
Some have mitral valve prolapse, a condition in which the heart mitral valve functions abnormally.
Diagnosis of Pectus Carinatum
Some patients may have a chest X-ray during their initial evaluation. This helps the surgeon screen for other chest abnormalities or scoliosis. In severe cases of breathing symptoms, a pulmonary function test may help to determine how much lung function is compromised.
A patient may also have an electrocardiogram (ECG or EKG) and an echocardiogram. An ECG is a test that records both normal and abnormal electrical activity of the heart. An echocardiogram is a procedure that uses sound waves to study the structures and function of the heart.
Treatment for Pectus Carinatum
Fortunately, because the chest wall in children and adolescents is very soft and flexible, pectus carinatum usually can be corrected with bracing. Less than 10 percent of children with pectus carinatum need surgery to correct the problem.
A New Way of Bracing
Cincinnati Children’s Hospital Center has been using bracing to treat children and adolescents with pectus carinatum since 1997. Cincinnati Children’s became one of the first hospitals in the country to offer a new bracing system called the FMF Dynamic Compressor. This light aluminum brace can be adjusted to fit the child and is easily hidden under clothing. The brace gives the right amount of pressure to slowly reshape the chest wall with little discomfort.
At the first visit, a pressure device is used to measure the chest wall to decide how much pressure is needed to fix the pectus carinatum. This helps the medical team develop a treatment plan, including how many hours a day the child will need to wear the brace and for how many months.
Children return to the clinic once a month for an exam and to see if changes need to be made to the brace. Once the pectus carinatum is fixed, the child wears the brace during the day and overnight for shorter periods of time. This helps keep the chest wall’s new shape.
Advantages of the FMF Dynamic Compressor
One of the benefits of this bracing system is that it objectively measures the pressure needed to fix the condition. This measurement guides treatment decisions and helps the medical team measure progress. It also allows the medical team to give an estimate of how long treatment will last and what the chest will look like afterward. Results usually happen faster with this system compared to other bracing systems.
The success rate for the FMF Dynamic Compressor is greater than 90 percent when children and adolescents wear it as directed. Younger children and teens, who usually have a very soft and flexible chest wall, tend to do best. In the rare event the chest wall is too stiff and does not respond to bracing, surgery is still an option.