Pulmonary Medicine

Publications

Acosta, MF; Muralidharan, P; Grijalva, CL; Abrahamson, MD; Hayes, D; Fineman, JR; Black, SM; Mansour, HM. Advanced therapeutic inhalation aerosols of a Nrf2 activator and RhoA/Rho kinase (ROCK) inhibitor for targeted pulmonary drug delivery in pulmonary hypertension: design, characterization, aerosolization, in vitro 2D/3D human lung cell cultures, and in vivo efficacy. Therapeutic Advances in Respiratory Disease. 2021; 15.

Amin, R. Beyond the Retrotrapezoid Nucleus in Congenital Central Hypoventilation Syndrome. American Journal of Respiratory and Critical Care Medicine. 2021.

Amorim, MR; Amin, R; Polotsky, VY. Of Mice and Babies: PHOX2B and Obstructive Apneas in Congenital Central Hypoventilation Syndrome. American Journal of Respiratory and Critical Care Medicine. 2021; 204:1128-1130.

Arora, K; Liyanage, P; Zhong, Q; Naren, AP. A SNARE protein Syntaxin 17 captures CFTR to potentiate autophagosomal clearance under stress. FASEB Journal. 2021; 35.

Arora, K; Yang, F; Brewington, J; McPhail, G; Cortez, AR; Sundaram, N; Ramananda, Y; Ogden, H; Helmrath, M; Clancy, JP; et al. Patient personalized translational tools in cystic fibrosis to transform data from bench to bed-side and back. American Journal of Physiology - Gastrointestinal and Liver Physiology. 2021; 320:G1123-G1130.

Bacharier, LB; Guilbert, TW; Jartti, T; Saglani, S. Which Wheezing Preschoolers Should be Treated for Asthma?. Journal of Allergy and Clinical Immunology: In Practice. 2021; 9:2611-2618.

Bailey, LC; Razzaghi, H; Burrows, EK; Bunnell, HT; Camacho, PE F; Christakis, DA; Eckrich, D; Kitzmiller, M; Lin, SM; Magnusen, BC; et al. Assessment of 135 794 Pediatric Patients Tested for Severe Acute Respiratory Syndrome Coronavirus 2 Across the United States. JAMA Pediatrics. 2021; 175:176-184.

Bates, AJ. Fundamentals of Fluid Dynamics. Clinical and Biomedical Engineering in the Human Nose. 2021.

Bates, AJ; Higano, NS; Woods, JC. Non-Bronchoscopic Assessment of the Airways. Diagnostic and Interventional Bronchoscopy in Children. 2021.

Bdaiwi, AS; Niedbalski, PJ; Hossain, MM; Willmering, MM; Walkup, LL; Wang, H; Thomen, RP; Ruppert, K; Woods, JC; Cleveland, ZI. Improving hyperpolarized 129 Xe ADC mapping in pediatric and adult lungs with uncertainty propagation. NMR in Biomedicine. 2021.

Beck, AF; Hartley, DM; Kahn, RS; Taylor, SC; Bishop, E; Rich, K; Saeed, MS; Schuler, CL; Seid, M; Cronin, SC; et al. Rapid, Bottom-Up Design of a Regional Learning Health System in Response to COVID-19. Mayo Clinic Proceedings. 2021; 96:849-855.

Beltran Ale, G; Pascoe, J; George, A; Woodward, J; Hossain, MM; Huang, G; Simakajornboon, N. Validation of pediatric sleep questionnaire in children with Chiari malformation and/or spina bifida with or without myelomeningocele. Sleep Medicine. 2021; 84:93-97.

Blankenship, CM; Hunter, LL; Feeney, MP; Cox, M; Bittinger, L; Garinis, AC; Lin, L; McPhail, G; Clancy, JP. Functional Impacts of Aminoglycoside Treatment on Speech Perception and Extended High-Frequency Hearing Loss in a Pediatric Cystic Fibrosis Cohort. American Journal of Audiology. 2021; 30:834-853.

Boat, T; Wesley Burks, A; Stoll, BJ. Challenges facing academic medicine: the Deans' view. Pediatric Research. 2021.

Boat, TF; Whitsett, JA. How Can the Pediatric Community Enhance Funding for Child Health Research?. JAMA Pediatrics. 2021; 175:1212-1214.

Borschuk, AP; Williams, SE; McClure, JM; Kendall, M; Mack, L; Coleman, M; Gurbani, N; Benscoter, D; Amin, R; Stark, LJ. A novel behavioral health program for family caregivers of children admitted to a transitional chronic ventilator unit. Pediatric Pulmonology. 2021; 56:1635-1643.

Brewington, J; Hong, J; Manfredi, C; Rab, A; Joshi, D; Linnemann, R; Streby, A; Stecenko, A; Ostmann, A; O’Shaughnessy, R; et al. 638: Demonstration of pharmacologic N1303 K CFTR rescue in heterologous and human tissue-based model systems. Journal of Cystic Fibrosis. 2021; 20.

Brewington, JJ; Benscoter, DT; Torres-Silva, CA; McHendry, CM; Lim, FY; Cortezzo, DM E; Hysinger, EB. Flexible Bronchoscopic Thrombus Cryoextraction in a Neonate on Extracorporeal Membrane Oxygenation. American Journal of Respiratory and Critical Care Medicine. 2021; 203:633-635.

Burg, G; Benscoter, D. Aspiration. Diagnostic and Interventional Bronchoscopy in Children. 2021.

Chen, L; Arens, R; Chidambaram, AG; Capponi, S; Alshawa, L; Claeys, TA; Hayes, D; Robinson, RT. Vaping Associated Pulmonary Nontuberculous Mycobacteria. Lung. 2021; 199:21-27.

Choi, T; Devries, M; Bacharier, LB; Busse, W; Camargo, CA; Cohen, R; Demuri, GP; Evans, MD; Fitzpatrick, AM; Gergen, PJ; et al. Enhanced Neutralizing Antibody Responses to Rhinovirus C and Age-Dependent Patterns of Infection. American Journal of Respiratory and Critical Care Medicine. 2021; 203:822-830.

Clayton von Allmen, D; Torres-Silva, C; Rutter, MJ. Factors associated with success following transcervical innominate artery suspension. International Journal of Pediatric Otorhinolaryngology. 2021; 150.

Cristea, AI; Baker, CD; Allen, J; Amin, R; Austin, ED; Cataletto, ME; Collaco, JM; Eldredge, LC; Fleck, RJ; Gelfand, A; et al. Outpatient Respiratory Management of Infants, Children, and Adolescents with Post-Prematurity Respiratory Disease: An Official American Thoracic Society Clinical Practice Guideline. American Journal of Respiratory and Critical Care Medicine. 2021; 204:e115-e133.

Critser, PJ; Evers, PD; Schneider, K; Hirsch, R; Taylor, MD; Woods, JC; Lang, SM. Echocardiography-derived septal curvature correlated with invasive hemodynamics in pediatric pulmonary hypertension. Journal of Echocardiography. 2021.

David, J; Berenblum Tobi, C; Kennedy, S; Jofriet, A; Huwe, M; Kelekian, R; Neihart, M; Spotts, M; Seid, M; Margolis, P. Sustainable generation of patient-led resources in a learning health system. Learning Health Systems. 2021; 5.

del Mar Romero Lopez, M; Carratola, M; Redmann, A; Evers, PD; Lim, FY; Kline-Fath, BM; Lehenbauer, DG; Rymeski, B; Torres-Silva, CA; Rutter, MJ. Right mainstem bronchial atresia successfully corrected with slide tracheobronchoplasty. Pediatric Pulmonology. 2021; 56:329-332.

DelRosso, LM; Picchietti, DL; Spruyt, K; Bruni, O; Garcia-Borreguero, D; Kotagal, S; Owens, JA; Simakajornboon, N; Ferri, R. Restless sleep in children: A systematic review. Sleep Medicine Reviews. 2021; 56.

Domany, KA; Huang, G; Hossain, MM; Schuler, CL; Somers, VK; Daniels, SR; Amin, R. Effect of Adenotonsillectomy on Cardiac Function in Children Age 5-13 Years With Obstructive Sleep Apnea. American Journal of Cardiology. 2021; 141:120-126.

Dong, M; Rodriguez, AV; Blankenship, CA; McPhail, G; Vinks, AA; Hunter, LL. Pharmacokinetic modelling to predict risk of ototoxicity with intravenous tobramycin treatment in cystic fibrosis. Journal of Antimicrobial Chemotherapy. 2021; 76:2923-2931.

Dournes, G; Hall, CS; Willmering, MM; Brody, AS; Macey, J; Bui, S; Denis-De-Senneville, B; Berger, P; Laurent, F; Benlala, I; et al. Artificial intelligence in CT for quantifying lung changes in the era of CFTR modulators. European Respiratory Journal, Supplement. 2021.

Dournes, G; Walkup, LL; Benlala, I; Willmering, MM; Macey, J; Bui, S; Laurent, F; Woods, JC. The Clinical Use of Lung MRI in Cystic Fibrosis: What, Now, How?. Chest. 2021; 159:2205-2217.

Duncan-Park, S; Dunphy, C; Becker, J; D’Urso, C; Annunziato, R; Blatter, J; Conrad, C; Goldfarb, SB; Hayes, D; Melicoff, E; et al. Remote intervention engagement and outcomes in the Clinical Trials in Organ Transplantation in Children consortium multisite trial. American Journal of Transplantation. 2021; 21:3112-3122.

Durfey, S; Radey, M; Hayden, H; Teresi, M; Kapnadak, S; Godwin, J; Boyken, L; Stroik, M; Vo, A; Singh, S; et al. 517: Regional evolution of Pseudomonas aeruginosa in the human host. Journal of Cystic Fibrosis. 2021; 20.

Dye, TJ; Hantragool, S; Carosella, C; Huang, G; Hossain, MM; Simakajornboon, N. Sleep disordered breathing in children receiving vagus nerve stimulation therapy. Sleep Medicine. 2021; 79:101-106.

Dye, TJ; Simakajornboon, N. Narcolepsy in Children: Sleep disorders in children, A rapidly evolving field seeking consensus. Pediatric Pulmonology. 2021.

Ehsan, Z; Weaver, KN; Pan, BS; Huang, G; Hossain, MM; Simakajornboon, N. Reply: Sleep Outcomes in Neonates with Pierre Robin Sequence Undergoing External Mandibular Distraction: A Longitudinal Analysis. Plastic and Reconstructive Surgery. 2021; 148:502e-503e.

Erkens, R; Esteban, Y; Towe, C; Schulert, G; Vastert, S. Pathogenesis and Treatment of Refractory Disease Courses in Systemic Juvenile Idiopathic Arthritis: Refractory Arthritis, Recurrent Macrophage Activation Syndrome and Chronic Lung Disease. Rheumatic Disease Clinics of North America. 2021; 47:585-606.

Feng, Y; Hayati, H; Bates, AJ; Walter, K; Matthias, L; Odo, B; Ramiro, O; Gerda, K. Clinical CFD Applications 2. Clinical and Biomedical Engineering in the Human Nose. 2021.

Filigno, S; Hente, E; Lisa, M; Siracusa, C. 335: Greater access to mental health care with CF team psychologist through telemedicine during COVID-19. Journal of Cystic Fibrosis. 2021; 20:s160-s160.

Fitch, T; Myers, KC; Dewan, M; Towe, C; Dandoy, C. Pulmonary Complications After Pediatric Stem Cell Transplant. Frontiers in Oncology. 2021; 11.

Foley, CL; Al Remeithi, SS; Towe, CT; Dauber, A; Backeljauw, PF; Tyzinski, L; Kumar, AR; Hwa, V. Developmental Adaptive Immune Defects Associated with STAT5B Deficiency in Three Young Siblings. Journal of Clinical Immunology. 2021; 41:136-146.

Forno, E; Bacharier, LB; Phipatanakul, W; Guilbert, TW; Cabana, MD; Ross, K; Covar, R; Gern, JE; Rosser, FJ; Blatter, J; et al. Effect of vitamin D3 supplementation on severe asthma exacerbations in children with asthma and low vitamin D levels: the VDKA randomized clinical trial. 2021.

Freedman, DS; Davies, AJ G; Kompaniyets, L; Lange, SJ; Goodman, AB; Phan, TL T; Cole, FS; Dempsey, A; Pajor, N; Eneli, I; et al. A Longitudinal Comparison of Alternatives to Body Mass Index Z-Scores for Children with Very High Body Mass Indexes. Journal of Pediatrics. 2021; 235:156-162.

Gaietto, K; Han, Y; Forno, E; Bacharier, LB; Phipatanakul, W; Guilbert, TW; Cabana, MD; Ross, K; Blatter, J; Acosta-Pérez, E; et al. Violence-related distress and lung function in two longitudinal studies of youth. European Respiratory Journal, Supplement. 2021.

Gajjala, PR; Kasam, RK; Soundararajan, D; Sinner, D; Huang, SK; Jegga, AG; Madala, SK. Dysregulated overexpression of Sox9 induces fibroblast activation in pulmonary fibrosis. JCI insight. 2021; 6.

Gajjala, PR; Madala, SK. Notch3: A New Culprit in Fibrotic Lung Disease. American Journal of Respiratory Cell and Molecular Biology. 2021; 64:403-404.

Gandhi, DB; Rice, A; Gunatilaka, CC; Higano, NS; Fleck, RJ; de Alarcon, A; Hart, CK; Kuo, IC; Amin, RS; Woods, JC; et al. Quantitative Evaluation of Subglottic Stenosis Using Ultrashort Echo Time MRI in a Rabbit Model. Laryngoscope. 2021; 131:E1971-E1979.

Gecili, E; Su, W; Brokamp, C; Andrinopoulou, ER; III, FJ L R; Pestian, T; Clancy, JP; Solomon, GM; Brewington, JJ; Szczesniak, RD. Rapid cystic fibrosis lung-function decline and in-vitro CFTR modulation. Journal of Cystic Fibrosis. 2021; 20:e69-e71.

Georgiopoulos, AM; Christon, LM; Filigno, SS; Mueller, A; Prieur, MG; Boat, TF; Smith, BA. Promoting emotional wellness in children with CF, part II: Mental health assessment and intervention. Pediatric Pulmonology. 2021; 56 Suppl 1:S107-S122.

Ghosh, M; Hill, CL; Alsudayri, A; Lallier, SW; Hayes, D; Wijeratne, S; Tan, ZH; Chiang, T; Mahoney, JE; Carraro, G; et al. Repeated injury promotes tracheobronchial tissue stem cell attrition. Stem cells translational medicine. 2021; 10:1696-1713.

Giambra, BK; Mangeot, C; Benscoter, DT; Britto, MT. A Description of Children Dependent on Long Term Ventilation via Tracheostomy and Their Hospital Resource Use. Journal of Pediatric Nursing. 2021; 61:96-101.

Ginsburg, D; Wee, CP; Reyes, MC; Brewington, JJ; Salinas, DB. When CFSPID becomes CF. Journal of Cystic Fibrosis. 2021.

Goralski, JL; Stewart, NJ; Woods, JC. Novel imaging techniques for cystic fibrosis lung disease. Pediatric Pulmonology. 2021; 56 Suppl 1:S40-S54.

Gunatilaka, CC; Hysinger, EB; Schuh, A; Gandhi, DB; Higano, NS; Xiao, Q; Hahn, AD; Fain, SB; Fleck, RJ; Woods, JC; et al. Neonates With Tracheomalacia Generate Auto-Positive End-Expiratory Pressure via Glottis Closure. Chest. 2021; 160:2168-2177.

Gupta, VS; Hayes, D; Hsu, SC; Tonna, JE; Rycus, PT; Bridges, BC; Diaban, F; Bosma, KJ; Bhatt, JM; Sakla, NM; et al. Extracorporeal Life Support for Respiratory Failure in Patients With Electronic Cigarette or Vaping Product Use-Associated Lung Injury. Critical Care Medicine. 2021.

Gurbani, N; Pascoe, JE; Katz, S; Sawnani, H. Sleep disordered breathing: Assessment and therapy in the age of emerging neuromuscular therapies. Pediatric Pulmonology. 2021; 56:700-709.

Hahn, AD; Malkus, A; Kammerman, J; Higano, N; Walkup, LL; Woods, J; Fain, SB. Effects of neonatal lung abnormalities on parenchymal R2 * estimates. Journal of Magnetic Resonance Imaging. 2021; 53:1853-1861.

Han, YY; Forno, E; Bacharier, LB; Phipatanakul, W; Guilbert, TW; Cabana, MD; Ross, K; Blatter, J; Rosser, FJ; Durrani, S; et al. Vitamin D supplementation, lung function and asthma control in children with asthma and low vitamin D levels. European Respiratory Journal, Supplement. 2021; 58.

Hardie, W; Powell, AW; Jenkins, TM; Foster, K; Tretter, JT; Fleck, RJ; Garcia, VF; Brown, RL. Ventilatory limitations are not associated with dyspnea on exertion or reduced aerobic fitness in pectus excavatum. Pediatric Pulmonology. 2021; 56:2911-2917.

Hardie, WD. Evaluation of a Summer Medical Student Research Program during a Pandemic. 2021; 2:172-175.

Hartley, DM; Keck, C; Havens, M; Margolis, PA; Seid, M. Measuring engagement in a collaborative learning health system: The case of ImproveCareNow. Learning Health Systems. 2021; 5.

Hartley, DM; Seid, M. Collaborative learning health systems: Science and practice. Learning Health Systems. 2021; 5.

Hayes, D; Darland, LK; Hjelm, MA; Mansour, HM; Wikenheiser-Brokamp, KA. To treat or not to treat: CFTR modulators after lung transplantation. Pediatric Transplantation. 2021; 25.

Hayes, D; Harhay, MO; Cherikh, WS; Chambers, DC; Perch, M; Khush, KK; Hsich, E; Potena, L; Sadavarte, A; Booker, S; et al. The International Thoracic Organ Transplant Registry of the International Society for Heart and Lung Transplantation: Twenty-fourth pediatric lung transplantation report - 2021; Focus on recipient characteristics. Journal of Heart Transplantation. 2021; 40:1023-1034.

Hayes, D; Rayner, RE; Hill, CL; Alsudayri, A; Tadesse, M; Lallier, SW; Parekh, H; Brock, GN; Cormet-Boyaka, E; Reynolds, SD. Airway epithelial stem cell chimerism in cystic fibrosis lung transplant recipients. Journal of Cystic Fibrosis. 2021; 20:165-172.

Hebbar, KB; Kasi, AS; Vielkind, M; McCracken, CE; Ivie, CC; Prickett, KK; Simon, DM. Mortality and Outcomes of Pediatric Tracheostomy Dependent Patients. Frontiers in Pediatrics. 2021; 9.

Hente, E; Strong, S; Siracusa, C; Hjelm, M; Bowdy, A; Tadesse, D; Hossain, M; Filigno, S; Boat, T. 315: Use of school intervention services and identification of educational risk in pediatric cystic fibrosis. Journal of Cystic Fibrosis. 2021; 20:s151-s151.

Hente, E; Weiland, J; Mullen, L; Hawke, J; Schuler, CL; Filigno, SS; Siracusa, C. Assessment of treatment burden and complexity in cystic fibrosis: A quality improvement project. Pediatric Pulmonology. 2021; 56:1992-1999.

Herbst, RB; Burkhardt, MC; Filigno, SS; Kerr, A; Boat, TF. Innovative pediatric resident training in behavioral health and communication: Pilot study results. Clinical Practice in Pediatric Psychology. 2021.

Higano, NS; Cao, X; Guo, J; Wang, X; Kroenke, CD; Filuta, AL; Bridges, JP; Woods, JC. Fetal lung development via quantitative biomarkers from diffusion MRI and histological validation in rhesus macaques. Journal of Perinatology. 2021.

Higano, NS; Ruoss, JL; Woods, JC. Modern pulmonary imaging of bronchopulmonary dysplasia. Journal of Perinatology. 2021; 41:707-717.

Higano, NS; Thomen, RP; Quirk, JD; Huyck, HL; Hahn, AD; Fain, SB; Pryhuber, GS; Woods, JC. Alveolar Airspace Size in Healthy and Diseased Infant Lungs Measured via Hyperpolarized 3He Gas Diffusion Magnetic Resonance Imaging. Neonatology. 2021; 117:704-712.

Huang, B; Chen, C; McPhail, G; Hayes, D; Wang, Z; Clancy, J; Szczesniak, R. 33: Hypertonic saline withdraw in CF patients while on ivacaftor: An analysis of the CF Foundation Patient Registry (CFFPR). Journal of Cystic Fibrosis. 2021; 20.

Huang, Y; Paul, G; Lee, J; Yarlagadda, S; McCoy, K; Naren, AP. Elexacaftor/Tezacaftor/Ivacaftor Improved Clinical Outcomes in a Patient with N1303K-CFTR Based on In Vitro Experimental Evidence. American Journal of Respiratory and Critical Care Medicine. 2021; 204:1231-1235.

Hysinger, EB. Evaluating Airway Dynamics. Diagnostic and Interventional Bronchoscopy in Children. 2021.

Hysinger, EB. Central airway issues in bronchopulmonary dysplasia. Pediatric Pulmonology. 2021; 56:3518-3526.

Hysinger, EB; Hart, CK; Burg, G; De Alarcon, A; Benscoter, D. Differences in Flexible and Rigid Bronchoscopy for Assessment of Tracheomalacia. Laryngoscope. 2021; 131:201-204.

Jaclyn, D; Andrew, NS; Ryan, P; Julianna, B; Christopher, S; Nauman, C; Powers, M; Gregory S, S; George M, S. Patient and family perceptions of telehealth as part of the cystic fibrosis care model during COVID-19. Journal of Cystic Fibrosis. 2021; 20:e23-e28.

Kearney, K; Lau, EM; Darley, D; Romfh, A; Bart, N; Kotlyar, E; Hayes, D; Khush, K; Keogh, A. Waitlist and post-transplant outcomes for eisenmenger syndrome: A comparison of transplant strategies. Journal of Heart Transplantation. 2021; 40:841-849.

Keck, C; Hartley, DM; Havens, M; Margolis, PA; Seid, M. Getting what is needed, when it's needed: Sharing information, knowledge, and know-how in a Collaborative Learning Health System. Learning Health Systems. 2021; 5.

Keegan, D; Meeker, J; Morgan, H; O’Shaughnessy, R; Brewington, J. 617: Chronic cAMP-dependent stimulation results in less activation of elexacaftor/tezacaftor/ivacaftor-corrected F508del CFTR. Journal of Cystic Fibrosis. 2021; 20.

Keegan, DE; Brewington, JJ. Nasal Epithelial Cell-Based Models for Individualized Study in Cystic Fibrosis. International Journal of Molecular Sciences. 2021; 22.

Kennedy, AA; Hart, CK; de Alarcon, A; Putnam, PE; von Allmen, D; Lehenbauer, D; Bryant, R; Torres-Silva, C; Rutter, MJ. Slide Tracheoplasty for Repair of Complex Tracheoesophageal Fistulas. Laryngoscope. 2021.

Khush, KK; Hsich, E; Potena, L; Cherikh, WS; Chambers, DC; Harhay, MO; Hayes, D; Perch, M; Sadavarte, A; Toll, A; et al. The International Thoracic Organ Transplant Registry of the International Society for Heart and Lung Transplantation: Thirty-eighth adult heart transplantation report - 2021; Focus on recipient characteristics. Journal of Heart Transplantation. 2021; 40:1035-1049.

Kim, H; Wikenheiser-Brokamp, K; Naren, A; Mun, K. 635: 3-D bioprinting of patient-derived submucosal gland to study mucociliary clearance. Journal of Cystic Fibrosis. 2021; 20:s301-s302.

Kocar, E; Lenarcic, T; Hodnik, V; Panevska, A; Huang, Y; Bajc, G; Kostanjšek, R; Naren, AP; Macek, P; Anderluh, G; et al. Crystal structure of RahU, an aegerolysin protein from the human pathogen Pseudomonas aeruginosa, and its interaction with membrane ceramide phosphorylethanolamine. Scientific Reports. 2021; 11.

Lannon, C; Schuler, CL; Seid, M; Provost, LP; Fuller, S; Purcell, D; Forrest, CB; Margolis, PA. A maturity grid assessment tool for learning networks. Learning Health Systems. 2021; 5.

Leong, A; Benscoter, D; Brewington, J; Torres-Silva, C; Wood, RE. Pediatric flexible airway endoscopy training during a pandemic and beyond: Bending the curve. Pediatric Pulmonology. 2021; 56:1386-1388.

Li, C; Zhao, K; Shusterman, D; Calmet, H; Bates, AJ; Siu, J; Douglas, R. Clinical CFD Applications 1. Clinical and Biomedical Engineering in the Human Nose. 2021.

Lin, NY; Roach, DJ; Willmering, MM; Walkup, LL; Hossain, MM; Desirazu, P; Cleveland, ZI; Guilbert, TW; Woods, JC. 129Xe MRI as a measure of clinical disease severity for pediatric asthma. Journal of Allergy and Clinical Immunology. 2021; 147:2146-2153.e1.

Lubert, AM; Alsaied, T; Trout, AT; Dillman, JR; Palermo, JJ; Eichelbrenner, F; Kleier, K; Lorts, A; Anwar, N; Schecter, MG; et al. Developing an adolescent and adult Fontan Management Programme. Cardiology in the Young. 2021; 1-6.

Melicoff, E; Hayes, D; Benden, C. Lung transplantation as an intervention for pediatric pulmonary hypertension. Pediatric Pulmonology. 2021; 56:587-592.

Mokhallati, N; Schuler, CL; Thomas, S; Hossian, MM; Guilbert, TW. Use of the composite asthma severity index in a pediatric subspecialty clinic. Annals of Allergy, Asthma and Immunology. 2021; 126:702-706.

Moutafidis, D; Gavra, M; Golfinopoulos, S; Oikonomopoulou, C; Kitra, V; Woods, JC; Kaditis, AG. Lung hyperinflation quantitated by chest CT in children with bronchiolitis obliterans syndrome following allogeneic hematopoietic cell transplantation. Clinical Imaging. 2021; 75:97-104.

Mukthapuram, S; Beebe, J; Tkach, JA; Arya, S; Haberman, B; Peiro, J; Lim, FY; Woods, JC; Kingma, PS. Magnetic Resonance Imaging Assessment of Pulmonary Vascularity in Infants with Congenital Diaphragmatic Hernia: A Novel Tool for Direct Assessment of Severity of Pulmonary Hypertension and Hypoplasia. Journal of Pediatrics. 2021; 239:89-94.

Mun, K; Kim, H; Wikenheiser-Brokamp, K; Abu-El-Haija, M; Nathan, J; Palermo, J; Naren, A. 621: Cystic fibrosis patient-specific organ on a chip to study CFTR-related disorders. Journal of Cystic Fibrosis. 2021; 20:s294-s295.

Muralidharan, P; Hayes, D; Fineman, JR; Black, SM; Mansour, HM. Advanced Microparticulate/Nanoparticulate Respirable Dry Powders of a Selective RhoA/Rho Kinase (Rock) Inhibitor for Targeted Pulmonary Inhalation Aerosol Delivery. Pharmaceutics. 2021; 13.

Niedbalski, PJ; Cleveland, ZI. Improved preclinical hyperpolarized 129 Xe ventilation imaging with constant flip angle 3D radial golden means acquisition and keyhole reconstruction. NMR in Biomedicine. 2021; 34.

Niedbalski, PJ; Cochran, AS; Freeman, MS; Guo, J; Fugate, EM; Davis, CB; Dahlke, J; Quirk, JD; Varisco, BM; Woods, JC; et al. Validating in vivo hyperpolarized 129 Xe diffusion MRI and diffusion morphometry in the mouse lung. Magnetic Resonance in Medicine. 2021; 85:2160-2173.

Niedbalski, PJ; Hall, CS; Castro, M; Eddy, RL; Rayment, JH; Svenningsen, S; Parraga, G; Zanette, B; Santyr, GE; Thomen, RP; et al. Protocols for multi-site trials using hyperpolarized 129 Xe MRI for imaging of ventilation, alveolar-airspace size, and gas exchange: A position paper from the 129 Xe MRI clinical trials consortium. Magnetic Resonance in Medicine. 2021; 86:2966-2986.

Niu, C; Xu, Y; Schuler, CL; Gu, L; Arora, K; Huang, Y; Naren, AP; Durrani, SR; Hossain, MM; Guilbert, TW. Evaluation of Risk Scores to Predict Pediatric Severe Asthma Exacerbations. Journal of Allergy and Clinical Immunology: In Practice. 2021; 9:4393-4401.e8.

Ogden, HL; Kim, H; Wikenheiser-Brokamp, KA; Naren, AP; Mun, KS. Cystic Fibrosis Human Organs-on-a-Chip. Micromachines. 2021; 12.

Ong, T; Onchiri, FM; Britto, MT; Heltshe, SL; Kessler, LG; Seid, M; Ramsey, BW. Impact of guideline-recommended dietitian assessments on weight gain in infants with cystic fibrosis. Journal of Cystic Fibrosis. 2021.

Pascoe, JE; Hantragool, S; Simakajornboon, N. Obstructive Sleep Apnea: Clinical Presentation and Differential Diagnosis. Pediatric Sleep Medicine. 2021.

Pennati, F; Walkup, LL; Chhabra, A; Towe, C; Myers, K; Aliverti, A; Woods, JC. Quantitative inspiratory-expiratory chest CT to evaluate pulmonary involvement in pediatric hematopoietic stem-cell transplantation patients. Pediatric Pulmonology. 2021; 56:1026-1035.

Perkins, RC; Davis, J; NeSmith, A; Bailey, J; Powers, MR; Chaudary, N; Siracusa, C; Uluer, A; Solomon, GM; Sawicki, GS. Favorable Clinician Acceptability of Telehealth as Part of the Cystic Fibrosis Care Model during the COVID-19 Pandemic. Annals of the American Thoracic Society. 2021; 18:1588-1592.

Phipatanakul, W; Mauger, DT; Guilbert, TW; Bacharier, LB; Durrani, S; Jackson, DJ; Martinez, FD; Fitzpatrick, AM; Cunningham, A; Kunselman, S; et al. Preventing asthma in high risk kids (PARK) with omalizumab: Design, rationale, methods, lessons learned and adaptation. Controlled Clinical Trials. 2021; 100.

Piccione, J; Hysinger, EB; Vicencio, AG. Pediatric advanced diagnostic and interventional bronchoscopy. Seminars in Pediatric Surgery. 2021; 30.

Pratt, J; Su, W; Hayes, D; Clancy, JP; Szczesniak, RD. An Animated Functional Data Analysis Interface to Cluster Rapid Lung Function Decline and Enhance Center-Level Care in Cystic Fibrosis. Journal of Healthcare Engineering. 2021; 2021.

Prieur, MG; Christon, LM; Mueller, A; Smith, BA; Georgiopoulos, AM; Boat, TF; Filigno, SS. Promoting emotional wellness in children with cystic fibrosis, Part I: Child and family resilience. Pediatric Pulmonology. 2021; 56 Suppl 1:S97-S106.

Ramananda, Y; Arora, K; Mun, K; Liyanage, P; Wikenheiser-Brokamp, K; Naren, A. 394: Role of adenylate cyclase 6 in mucociliary clearance. Journal of Cystic Fibrosis. 2021; 20.

Ramsey, RR; Guilbert, TW. Exciting Era of Sensor-Based Electronic Monitoring of Adherence in Pediatric Asthma. Pediatrics. 2021; 147.

Ramsey, RR; Plevinsky, JM; Milgrim, L; Hommel, KA; McDowell, KM; Shepard, J; Guilbert, TW. Feasibility and preliminary validity of mobile spirometry in pediatric asthma. Journal of Allergy and Clinical Immunology: In Practice. 2021; 9:3821-3823.

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